Consensus document on autosomal dominant polycystic kindey disease from the Spanish Working Group on Inherited Kindey Diseases. Review 2020
Mostra el registre complet Registre parcial de l'ítem
- dc.contributor.author Ars, Elisabet
- dc.contributor.author Bernis, Carmen
- dc.contributor.author Fraga, Gloria
- dc.contributor.author Furlano, Mónica
- dc.contributor.author Martínez, Víctor
- dc.contributor.author Martins, Judith
- dc.contributor.author Ortiz, Alberto
- dc.contributor.author Pérez-Gómez, Maria Vanessa
- dc.contributor.author Rodríguez-Pérez, José Carlos
- dc.contributor.author Sans Atxer, Laia
- dc.contributor.author Torra, Roser
- dc.date.accessioned 2023-04-19T11:41:37Z
- dc.date.available 2023-04-19T11:41:37Z
- dc.date.issued 2022
- dc.description.abstract Autosomal dominant polycystic kidney disease (ADPKD) is the most frequent cause of genetic renal disease and accounts for 6-10% of patients on kidney replacement therapy (KRT). Very few prospective, randomized trials or clinical studies address the diagnosis and management of this relatively frequent disorder. No clinical guidelines are available to date. This is a revised consensus statement from the previous 2014 version, presenting the recommendations of the Spanish Working Group on Inherited Kidney Diseases, which were agreed to following a literature search and discussions. Levels of evidence mostly are C and D according to the Centre for Evidence-Based Medicine (University of Oxford). The recommendations relate to, among other topics, the use of imaging and genetic diagnosis, management of hypertension, pain, cyst infections and bleeding, extra-renal involvement including polycystic liver disease and cranial aneurysms, management of chronic kidney disease (CKD) and KRT and management of children with ADPKD. Recommendations on specific ADPKD therapies are provided as well as the recommendation to assess rapid progression.
- dc.format.mimetype application/pdf
- dc.identifier.citation Ars E, Bernis C, Fraga G, Furlano M, Martínez V, Martins J, Ortiz A, Pérez-Gómez MV, Rodríguez-Pérez JC, Sans L, Torra R; en nombre del grupo de trabajo de Enfermedades Renales Hereditarias de la Sociedad Española de Nefrología. Consensus document on autosomal dominant polycystic kindey disease from the Spanish Working Group on Inherited Kindey Diseases. Review 2020. Nefrologia (Engl Ed). 2022 Jul-Aug;42(4):367-89. DOI: 10.1016/j.nefroe.2022.11.011
- dc.identifier.doi http://dx.doi.org/10.1016/j.nefroe.2022.11.011
- dc.identifier.issn 2013-2514
- dc.identifier.uri http://hdl.handle.net/10230/56503
- dc.language.iso eng
- dc.publisher Elsevier
- dc.relation.ispartof Nefrologia (Engl Ed). 2022 Jul-Aug;42(4):367-89
- dc.rights © 2021 Sociedad Española de Nefrología. Published by Elsevier España, S.L.U. This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
- dc.rights.accessRights info:eu-repo/semantics/openAccess
- dc.rights.uri http://creativecommons.org/licenses/by-nc-nd/4.0/
- dc.subject.keyword ADPKD
- dc.subject.keyword Autosomal dominant polycystic kidney disease
- dc.subject.keyword Consensus
- dc.subject.keyword Management
- dc.subject.keyword Progression
- dc.subject.keyword Recommendations
- dc.title Consensus document on autosomal dominant polycystic kindey disease from the Spanish Working Group on Inherited Kindey Diseases. Review 2020
- dc.type info:eu-repo/semantics/article
- dc.type.version info:eu-repo/semantics/publishedVersion