Ariceta, GemaBuj, María JoséFurlano, MónicaMartínez, VíctorMatamala, AnnaMorales, MontserratRobles, Nicolás RobertoSans Atxer, LaiaVillacampa, FelipeTorra, Roser2021-03-102021-03-102020Ariceta G, Buj MJ, Furlano M, Martínez V, Matamala A, Morales M, et al. Recomendaciones de manejo de la afectación renal en el complejo esclerosis tuberosa. Nefrologia. 2020 Mar-Apr; 40(2):142-51. DOI: 10.1016/j.nefro.2019.07.0020211-6995http://hdl.handle.net/10230/46712Tuberous sclerosis complex (TSC) is a rare, hereditary, multisystemic disease with a broad phenotypic spectrum. Its management requires the collaboration of multiple specialists. Just as in the paediatric age, the paediatric neurologist takes on special importance; in adulthood, renal involvement is the cause of the greatest morbidity and mortality. There are several recommendations on the general management of patients with TSC but none that focuses on renal involvement. These recommendations respond to the need to provide guidelines to facilitate a better knowledge and diagnostic-therapeutic management of the renal involvement of TSC through a rational use of complementary tests and the correct use of available treatments. Their elaboration has been based on consensus within the hereditary renal diseases working group of the SEN/REDINREN (Spanish Society of Nephrology/Kidney Research Network). It has also counted on the participation of non-nephrologist specialists in TSC in order to expand the vision of the disease.application/pdfspa0211-6995/© 2019 Publicado por Elsevier España, S.L.U. en nombre de Sociedad Española de Nefrología. Este es un articulo Open Access bajo la licencia CC BY-NC-ND (http://creativecommons.org/licenses/by-nc-nd/4.0/).info:eu-repo/semantics/articlehttp://dx.doi.org/10.1016/j.nefro.2019.07.002AngiomiolipomasAngiomyolipomasContiguous gene syndromeCystsEnfermedad renal poliquísticaEsclerosis tuberosaPolycystic kidney diseaseProteína mTORQuistesSíndrome del gen contiguoTuberous sclerosismTOR proteininfo:eu-repo/semantics/openAccess